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CASE REPORT
A case of Behçet disease with vitiligo, psoriasis and scleritis
1
Department of Rheumatology, School of Medicine, Collegium Medicum, University of Warmia and Mazury in Olsztyn, Poland
2
Department of Ophthalmology, Municipal Hospital, Olsztyn, Poland
3
Department of Dermatology, Sexually Transmitted Diseases and Clinical Immunology, School of Medicine, Collegium Medicum, University of Warmia and Mazury in Olsztyn, Poland
Submission date: 2021-03-13
Final revision date: 2021-10-13
Acceptance date: 2021-10-13
Online publication date: 2021-11-16
Corresponding author
Grzegorz Chmielewski
Department of Rheumatology, School of Medicine, Collegium Medicum, University of Warmia and Mazury, Wojska Polskiego 30, 10-229 Olsztyn, Poland.
Department of Rheumatology, School of Medicine, Collegium Medicum, University of Warmia and Mazury, Wojska Polskiego 30, 10-229 Olsztyn, Poland.
Pol. Ann. Med. 2022;29(2):211-215
KEYWORDS
TOPICS
ABSTRACT
Introduction:
Behçet disease (BD) is a rare systemic vasculitis of unknown aetiology, which can involve different size arteries and veins. The syndrome is characterized by oral aphthous ulcers, genital ulcers, skin and ocular lesions, arthritis, gastrointestinal ulcers, and neurological signs.
Aim:
The aim of this paper is to discuss comorbidity of BD with other autoimmune diseases referring to a clinical case report.
Case study:
The study presents a case of BD concurrent with vitiligo, psoriasis and scleritis in a 22-year-old patient.
Results and discussion:
The aetiology and pathogenesis of BDare unknown. The presented case of BD was accompanied by psoriasis, nodular scleritis, and vitiligo, which is uncommon. In Poland, since the disease is rare and only single cases have been identified, the precise epidemiology is unknown. Currently, more cases are being diagnosed.
Conclusions:
Due to nonspecific symptoms and rarity in some countries, BD diagnosis can be delayed, which may have a negative effect on a patient’s life quality. Further studies exploring the correlation between BD, psoriasis, vitiligo, and nodular scleritis are needed to better understand the pathogenesis and relationship between the diseases.
Behçet disease (BD) is a rare systemic vasculitis of unknown aetiology, which can involve different size arteries and veins. The syndrome is characterized by oral aphthous ulcers, genital ulcers, skin and ocular lesions, arthritis, gastrointestinal ulcers, and neurological signs.
Aim:
The aim of this paper is to discuss comorbidity of BD with other autoimmune diseases referring to a clinical case report.
Case study:
The study presents a case of BD concurrent with vitiligo, psoriasis and scleritis in a 22-year-old patient.
Results and discussion:
The aetiology and pathogenesis of BDare unknown. The presented case of BD was accompanied by psoriasis, nodular scleritis, and vitiligo, which is uncommon. In Poland, since the disease is rare and only single cases have been identified, the precise epidemiology is unknown. Currently, more cases are being diagnosed.
Conclusions:
Due to nonspecific symptoms and rarity in some countries, BD diagnosis can be delayed, which may have a negative effect on a patient’s life quality. Further studies exploring the correlation between BD, psoriasis, vitiligo, and nodular scleritis are needed to better understand the pathogenesis and relationship between the diseases.
FUNDING
None declared.
CONFLICT OF INTEREST
None declared.
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