Introduction: Congenital transsphenoidal meningocele is extremely rare.
Aim: We present a newborn who was found to have a large midline cystic mass protruding from a cleft palate.
Case study: Radiological imaging showed a large cerebrospinal fluid mass herniating through a large anterior cranial fossa defect into the sphenoid sinus with extension to the nasal cavity through a cleft palate into the oral cavity.
Results and discussion: A bifrontal craniotomy and decompression of meningocele with dura repair was performed.
Conclusions: The child was discharged healthy postoperatively and on monthly follow-up and subsequently thriving well with improving neurological recovery.
FUNDING
None declared.
CONFLICT OF INTEREST
No conflict of interest declared.
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