CASE REPORT
Congenital transsphenoidal meningocele in a newborn: A case report
 
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1
Department of Otorhinolaryngology-Head & Neck Surgery, Universiti Sains Malaysia Health Campus, Kubang Kerian, Kelantan, Malaysia
 
2
Department of Neurosurgery, Universiti Sains Malaysia Health Campus, Kubang Kerian, Kelantan, Malaysia
 
 
Submission date: 2023-11-28
 
 
Final revision date: 2023-12-20
 
 
Acceptance date: 2023-12-20
 
 
Online publication date: 2024-02-26
 
 
Corresponding author
Azliana Aziz   

Department of Otorhinolaryngology-Head & Neck Surgery, Universiti Sains Malaysia Health Campus, Kubang Kerian, Kelantan., Malaysia
 
 
Pol. Ann. Med. 2024;31(1):53-58
 
KEYWORDS
TOPICS
ABSTRACT
Introduction:
Congenital transsphenoidal meningocele is extremely rare.

Aim:
We present a newborn who was found to have a large midline cystic mass protruding from a cleft palate.

Case study:
Radiological imaging showed a large cerebrospinal fluid mass herniating through a large anterior cranial fossa defect into the sphenoid sinus with extension to the nasal cavity through a cleft palate into the oral cavity.

Results and discussion:
A bifrontal craniotomy and decompression of meningocele with dura repair was performed.

Conclusions:
The child was discharged healthy postoperatively and on monthly follow-up and subsequently thriving well with improving neurological recovery.

FUNDING
None declared.
CONFLICT OF INTEREST
No conflict of interest declared.
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