CASE REPORT
Congenital transsphenoidal meningocele in a newborn: A case report
 
More details
Hide details
1
Department of Otorhinolaryngology-Head & Neck Surgery, Universiti Sains Malaysia Health Campus, Kubang Kerian, Kelantan, Malaysia
 
2
Department of Neurosurgery, Universiti Sains Malaysia Health Campus, Kubang Kerian, Kelantan, Malaysia
 
 
Submission date: 2023-11-28
 
 
Final revision date: 2023-12-20
 
 
Acceptance date: 2023-12-20
 
 
Online publication date: 2024-02-26
 
 
Corresponding author
Azliana Aziz   

Department of Otorhinolaryngology-Head & Neck Surgery, Universiti Sains Malaysia Health Campus, Kubang Kerian, Kelantan., Malaysia
 
 
Pol. Ann. Med. 2024;31(1):53-58
 
KEYWORDS
TOPICS
ABSTRACT
Introduction:
Congenital transsphenoidal meningocele is extremely rare.

Aim:
We present a newborn who was found to have a large midline cystic mass protruding from a cleft palate.

Case study:
Radiological imaging showed a large cerebrospinal fluid mass herniating through a large anterior cranial fossa defect into the sphenoid sinus with extension to the nasal cavity through a cleft palate into the oral cavity.

Results and discussion:
A bifrontal craniotomy and decompression of meningocele with dura repair was performed.

Conclusions:
The child was discharged healthy postoperatively and on monthly follow-up and subsequently thriving well with improving neurological recovery.

FUNDING
None declared.
CONFLICT OF INTEREST
No conflict of interest declared.
 
REFERENCES (18)
1.
Kälién B, Robert E, Harris J. Associated malformations in infants and fetuses with upper or lower neural tube defects. Teratology. 1998;57(2):56–63. https://doi.org/10.1002/(sici)....
 
2.
Schick B, Brors D, Prescher A. Sternberg's canal-cause of congenital sphenoidal meningocele. Eur Arch Otorhinolaryngol. 2000;257(8):430–432. https://doi.org/10.1007/s00405....
 
3.
Barañano CF, Curé J, Palmer JN, Woodworth BA. Sternberg's canal: fact or fiction? Am J Rhinol Allergy. 2009;23(2):167–171. https://doi.org/10.2500/ajra.2....
 
4.
Sternberg M. A previously undescribed canal in the sphenoid bone of humans. Anat Anz. 1888;3:784–785.
 
5.
Cruz e Silva V, Luís A, Mora Féria R, et al. Transsphenoidal meningoencephalocele protruding into the nasal cavity. BJR Case Rep. 2016;3(2):20160082. https://doi.org/10.1259/bjrcr.....
 
6.
Blaivie C, Lequeux T, Kampouridis S, Louryan S, Saussez S. Congenital transsphenoidal meningocele: case report and review of the literature. Am J Otolaryngol. 2006;27(6):422–424. https://doi.org/10.1016/j.amjo....
 
7.
Katori Y, Kawamoto A, Cho KH, et al. Transsphenoidal meningocele: an anatomical study using human fetuses including report of a case. Eur Arch Otorhinolaryngol. 2013;270(10):2729–2736. https://doi.org/10.1007/s00405....
 
8.
Kahyaoglu, O, Cavusoglu, H, Musluman, AM, et al. Transsellar transsphenoidal rhino-oral encephalocele. Turk Neurosurg. 2007;17:264–268.
 
9.
Okano S, Tanaka R, Okayama A, et al. Congenital basal meningoceles with different outcomes: a case series. J Med Case Rep. 2017;11(1):359. https://doi.org/10.1186%2Fs132....
 
10.
Das S, Collins T. True transsphenoidal meningoencephalocele. Headache. 2017;57(7):1154–1155. https://doi.org/10.1111/head.1....
 
11.
Meder JF, Melanson D, Ethier R. Persistent craniopharyngeal canal. Apropos of 3 radiologic studies. J Neuroradiol. 1983;10(3):265–274.
 
12.
Settecase F, Harnsberger HR, Michel MA, Chapman P, Glastonbury CM. Spontaneous lateral sphenoid cephaloceles: anatomic factors contributing to pathogenesis and proposed classification. AJNR Am J Neuroradiol. 2014;35(4):784–789. https://doi.org/10.3174/ajnr.a....
 
13.
Thompson HM, Schlosser RJ, McCarty Walsh E, et al. Current management of congenital anterior cranial base encephaloceles. Int J Pediatr Otorhinolaryngol. 2020;131:109868. https://doi.org/10.1016/j.ijpo....
 
14.
Thompson HM, Cho DY, Riley KO, Grayson JW, Woodworth BA. Systematic review of anterior congenital cephaloceles: open vs endoscopic repair. Int Forum Allergy Rhinol. 2020;10(12):1334–1336. https://doi.org/10.1002/alr.22....
 
15.
Demidowicz R, Jarmołowicz N, Grzybowska S, Zajączkiewicz H, Kukwa A. Bicoronal approach in managing frontal sinus osteoma – case report. Pol Ann Med. 2018;25(1):117–120. https://doi.org/10.29089/2017.....
 
16.
Kennedy, EM, Gruber, DP, Billmire, DA, Crone, KR. Transpalatal approach for the extracranial surgical repair of transsphenoidal cephaloceles in children. J Neurosurg. 1997;87:677–681. https://doi.org/10.3171/jns.19....
 
17.
Zoli M, Farneti P, Ghirelli M, et al. Meningocele and meningoencephalocele of the lateral wall of sphenoidal sinus. World Neurosurg. 2017;107:1038. https://doi.org/10.1016/j.wneu....
 
18.
Hoff SR, Edwards MS, Bailey CM, Koltai PJ. The transpalatal approach to repair of congenital Basal skull base cephaloceles. J Neurol Surg B Skull Base. 2014;75(2):96–103. https://doi.org/10.1055%2Fs-00....
 
Journals System - logo
Scroll to top