Introduction:
Teratoma is a rarely occurring neoplasm characterized by an abnormal growth of tissues deriving from three germinal layers: endoderm, mesoderm and ectoderm. Liver is a very rare site for teratoma, as only 28 hepatic teratomas were reported, including 21 in children. Furthermore, teratoma of the liver accounts for less than 1% of all hepatic neoplasms and the majority of these cases occurred in female children below the age of three. Hence, our case is particularly unique.

Aim:
The aim of this paper was to report a rare case of a teratoma of the hepatic hilum.

Case study:
We report a case of a 12-year-old boy suffering from abdominal pain since the age of 2. Medical imaging revealed an abdominal cyst and after the surgery and histological examination mature teratoma of the hepatic hilum was diagnosed.

Results and discussion:
Hilum is particularly unique localization for a liver teratoma, as so far only one such case has been reported. The histology showed a mixture of mature tissues, and no immature elements were found. Thus, histology was typical for Teratoma maturum.

Conclusions:
The case described here represent a rare case of hepatic teratoma with particularly unique localization in the hepatic hilum.